Abstract
Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) is a right ventricular disease caused by desmosomal gene mutations leading to fibro-fatty replacement of the myocardium causing ventricular arrhythmias such as ventricular tachycardia (VT). A 59-year-old female presented with new onset VT manifesting as shortness of breath and chest discomfort. Diagnostic workup revealed right ventricular dilation/dysfunction on echocardiogram, VT with left bundle branch block (LBBB) and diffuse T wave inversions (TWIs) on EKG. She was discharged with a diagnosis of ARVC. Later, she developed VT storm, treated with epi-endocardial ablation for complete resolution of recurrent VT. Our case demonstrates the rare presentation of ARVC as ventricular storm and the various management strategies such as antiarrhythmics, automated implantable cardioverter-defibrillator (AICD) and ablation procedures.
Recommended Citation
Thomas, Shon; Jackubowski, Jaclynn; Ismair, Kevin; Chang, Jeremiah; and Kuhnlein, Jerome
()
"Arrhythmogenic Right Ventricular Cardiomyopathy Presenting With VT Electrical,"
Journal of Community Hospital Internal Medicine Perspectives: Vol. 15:
Iss.
1, Article 15.
DOI: 10.55729/2000-9666.1432
Available at:
https://scholarlycommons.gbmc.org/jchimp/vol15/iss1/15
