Solid pseudopapillary neoplasms (SPNs) are exceedingly rare type of exocrine pancreatic malignancy, representing only 0.9%-2.7% of all exocrine pancreatic malignancies. They predominantly affect young women and unlike other pancreatic malignancies, they have excellent prognoses with 5-year survival following surgical resection approaching 97%. Given the rarity of the disease, little is known about their histopathogenesis as they do not harbor similar genetic mutational abnormalities like other pancreatic tumors. We describe a rare case of SPN in a young female who was found to have the rare diagnosis during the work up for deranged liver function tests.
Adhikari, Biplov; Jones, Robert; and Haas, Christopher James
"Solid Pseudo-papillary Neoplasia: A Rare Malignancy of the Pancreas,"
Journal of Community Hospital Internal Medicine Perspectives: Vol. 13:
6, Article 8.
Available at: https://scholarlycommons.gbmc.org/jchimp/vol13/iss6/8