Solid Pseudo-papillary Neoplasia: A Rare Malignancy of the Pancreas

Authors

Biplov Adhikari, Medstar Health Internal Medicine Residency Training Program, Baltimore, MD, USAFollow
Robert Jones, Department of Pathology, Medstar Franklin Square Medical Center, Baltimore, MD
Christopher James Haas, Department of Medicine, Georgetown University Medical Center, Washington, DC

Abstract

Solid pseudopapillary neoplasms (SPNs) are exceedingly rare type of exocrine pancreatic malignancy, representing only 0.9%-2.7% of all exocrine pancreatic malignancies. They predominantly affect young women and unlike other pancreatic malignancies, they have excellent prognoses with 5-year survival following surgical resection approaching 97%. Given the rarity of the disease, little is known about their histopathogenesis as they do not harbor similar genetic mutational abnormalities like other pancreatic tumors. We describe a rare case of SPN in a young female who was found to have the rare diagnosis during the work up for deranged liver function tests.

Recommended Citation

Adhikari, Biplov; Jones, Robert; and Haas, Christopher James (2023) "Solid Pseudo-papillary Neoplasia: A Rare Malignancy of the Pancreas," Journal of Community Hospital Internal Medicine Perspectives: Vol. 13: Iss. 6, Article 8.
DOI: 10.55729/2000-9666.1254
Available at: https://scholarlycommons.gbmc.org/jchimp/vol13/iss6/8